Abstract

Mounier-Kuhn syndrome (MKS), or tracheobronchomegaly, is a rare congenital disorder characterized by the abnormal dilation of the trachea and bronchi, often leading to recurrent respiratory infections and chronic lung disease. We report the case of a 65-year-old male who presented with a 30-year history of chronic cough, sputum production, and shortness of breath. The patient, a long-term smoker, underwent chest computed tomography (CT), which revealed bronchiectasis, emphysema, thickened pleura, and multiple tracheal diverticula, along with significant dilation of the trachea and both main bronchi. Pulmonary function testing showed moderate-to-severe obstructive dysfunction, and the diagnosis of MKS was confirmed. The patient was treated with antibiotics and bronchodilators in an outpatient setting after declining hospitalization. Additionally, MKS is often underdiagnosed due to its rarity, but should be considered in patients with recurrent respiratory infections and airway obstruction. Diagnosis is typically based on chest CT, with characteristic tracheal and bronchial dilation. Treatment is primarily supportive, focusing on infection control and airway management. This case highlights the need for increased awareness of MKS for timely diagnosis and intervention.